Contributions of musical approaches to the development of auditory, speech, and language skills of children and adolescents with cochlear implants: a scoping review / Contributos das abordagens musicais no desenvolvimento das habilidades auditivas, de fala e linguagem de crianças e adolescentes usuários de implante coclear: uma revisão de escopo

ABSTRACT Purpose: to map, through a scoping review, the contributions of musical approaches to developing auditory, speech, and language skills in children and adolescents using cochlear implants (CIs). Methods: a review conducted following the Preferred Reporting Items for Systematic Reviews and Meta-Analyses-Extension for Scoping Reviews (PRISMA-ScR) and registered in PROSPERO, under the review registration number CRD42020205581. A bibliographic search was carried out in databases in 2020 and updated in August 2023. No date or language limits were applied. Literature Review: altogether, 1,351 studies were found through the search strategy. After the eligibility assessment based on the PCC strategy, 11 studies were selected and analyzed in full text. Conclusion: the studies have demonstrated that musical approaches contribute to developing auditory, speech, and language skills in children and adolescents using CIs.

RESUMO Objetivo: mapear, por meio de uma revisão de escopo, os contributos das abordagens musicais para o desenvolvimento das habilidades auditivas, de fala e linguagem de crianças e adolescentes usuários de implante coclear (IC). Métodos: esta revisão foi conduzida de acordo com o Preferred Reporting Items for Systematic Reviews and the Meta-Analyses extension for Scoping Reviews (PRISMA-ScR) e registrada no PROSPERO com o número de registro da revisão: CRD42020205581. Foi realizada uma busca bibliográfica nas bases de dados em 2020 e atualizada em agosto de 2023. Não foram aplicados limites de data e idioma. Revisão da Literatura: foram encontrados 1.351 estudos por meio da estratégia de busca e após a avaliação de elegibilidade baseada pela estratégia PCC, 11 estudos foram selecionados e analisados na íntegra. Conclusão: os estudos demonstraram que as abordagens musicais contribuem para o desenvolvimento das habilidades auditivas, de fala e linguagem de crianças e adolescentes usuários de IC.

Hearing health educational interventions for school students / Intervenções educativas em saúde auditiva para escolares

ABSTRACT Purpose: to implement and assess hearing health interventions for school students, using Dangerous Decibels® Program activities in partnership with the Young Doctor Project, approaching noise-induced hearing loss prevention. Methods: the study encompassed 41 students, aged 12 to 14 years, from two schools in inland São Paulo and a social institution for public school students. Activities were based on the Young Doctor Project and the Dangerous Decibels® Brazil Program. The students answered a questionnaire administered in three situations: before the intervention (pre), right after the intervention (post), and 4 months after the intervention. The ANOVA, Friedman (p < 0.001), and Tukey´s (p < 0.05) statistical tests were used. Results: the 41 students who participated in the program were protagonists of knowledge, spreading the content they learned to another 954 students in the three schools through cultural workshops. The analysis of program effectiveness revealed improved results right after the intervention and 4 months afterward. Conclusion: combining these two programs encouraged the protagonism of young people to increase their involvement with the community. Moreover, the students changed their attitude toward potentially dangerous sounds.

RESUMO Objetivo: implementar e avaliar intervenções em saúde auditiva para escolares, utilizando as atividades do Programa Dangerous Decibels ®, em parceria com o Projeto Jovem Doutor, abordando aspectos preventivos da perda auditiva induzida por níveis de pressão sonora elevados. Métodos: participaram do estudo 41 escolares, com idade entre 12 e 14 anos, de duas escolas no interior de São Paulo e uma Instituição Social direcionada a estudantes de escolas públicas. As atividades foram baseadas no Projeto Jovem Doutor e no programa Dangerous Decibels ® Brasil. Os escolares responderam a um questionário aplicado em três situações, antes da intervenção (pré), logo após a intervenção (pós) e quatro meses após a intervenção. Foram utilizados os testes estatísticos ANOVA, FRIEDMAN; p<0,001 e TUKEY; p<0,05. Resultados: os 41 escolares que participaram do programa atuaram como protagonistas do conhecimento, multiplicando o conteúdo aprendido através das oficinas culturais, envolvendo 954 escolares das três escolas. Ao analisar a eficácia do programa, observou-se melhora nos resultados logo após a intervenção e, também, após 4 meses. Conclusão: a união desses dois programas incentivou o protagonismo juvenil, objetivando o maior envolvimento dos estudantes junto da comunidade. Foi possível observar a mudança de atitude dos escolares frente aos sons potencialmente perigosos.

Preliminary Study of the Applicability of Software in the Investigation of Sustained Auditory Attention

Abstract Introduction The use of auditory behavioral tests, which specifically assess sustained attention, is necessary, due to its relationship with learning, language production, cognitive development and school performance. Objective To evaluate how children performed using software developed to investigate the ability of sustained auditory attention, and to compare the scores obtained in this format with those of the original, non-computerized test. Methods This cross-sectional study included 52 children of both genders, aged 6 to 11 years, with normal hearing and no history of complaints regarding inattention and/or hyperactivity. The computerized test was administered to all 52 children. The total error score (inattention and impulsivity) and the vigilance decrement were used to define the children's performance when using the software. The scores obtained in the two formats (computer software and original on compact disc) were then compared. Results Statistically significant differences were found in the scores for innattention, impulsivity, and total error score (inattention and impulsivity) when comparing genders, and a negative correlation coefficient was found when comparing ages. Increased scores were found for all variables of the sustained auditory attention ability test (SAAAT) compared with the original format. Conclusion Females performed worse than males in all aspects except for vigilance decrement when using the SAAATsoftware developed to evaluate the ability of SAAAT vigilance; younger children made more errors when using the SAAAT software; inattention errors were more frequent than impulsivity. Overall, higher values were obtained using the SAAAT software, when compared with the original version.

Preliminary Study of the Applicability of Software in the Investigation of Sustained Auditory Attention.

Introduction The use of auditory behavioral tests, which specifically assess sustained attention, is necessary, due to its relationship with learning, language production, cognitive development and school performance. Objective To evaluate how children performed using software developed to investigate the ability of sustained auditory attention, and to compare the scores obtained in this format with those of the original, non-computerized test. Methods This cross-sectional study included 52 children of both genders, aged 6 to 11 years, with normal hearing and no history of complaints regarding inattention and/or hyperactivity. The computerized test was administered to all 52 children. The total error score (inattention and impulsivity) and the vigilance decrement were used to define the children's performance when using the software. The scores obtained in the two formats (computer software and original on compact disc) were then compared. Results Statistically significant differences were found in the scores for innattention, impulsivity, and total error score (inattention and impulsivity) when comparing genders, and a negative correlation coefficient was found when comparing ages. Increased scores were found for all variables of the sustained auditory attention ability test (SAAAT) compared with the original format. Conclusion Females performed worse than males in all aspects except for vigilance decrement when using the SAAAT software developed to evaluate the ability of SAAAT vigilance; younger children made more errors when using the SAAAT software; inattention errors were more frequent than impulsivity. Overall, higher values were obtained using the SAAAT software, when compared with the original version.

Oral language skills in Brazilian children with obstructive sleep apnea.

BACKGROUND: Obstructive sleep apnea (OSA) is associated with a negative impact on neurocognitive development in children. Receptive/expressive oral language is a complex process, with limited investigations on the repercussion of OSA. This study aimed to analyze receptive and expressive oral language skills in children with obstructive sleep apnea (OSA). METHODOLOGY: This study included 52 children (27 females, 51.92 %) with a mean age of 7 ± 2 years (age range of 4-11 years), which underwent type 3 polysomnography (PSG). The participants were divided into N-OSA (n = 16) and OSA (n = 36) groups based on the apnea-hypopnea index. The speech-language therapist evaluated hearing and oral language for phonology, expressive semantics, syntax, receptive semantics (Peabody Image Vocabulary Test), pragmatics, and understanding of verbal instructions (Token Test). RESULTS: Oral language assessments showed a difference in the pragmatics subsystem (p = 0.047), with positive correlation between OSA severity and oral language functions such as pragmatics and syntax (desaturation index, p = 0.045). CONCLUSION: Obstructive sleep apnea (OSA) had a negative impact on oral language skills, including the syntax and pragmatics subsystems.

Auditory and language skills in children with cleft lip and palate.

OBJECTIVES: to investigate auditory and language skills in children with repaired cleft lip and palate. METHODS: The sample was composed of 22 children registered at the hospital where the study was conducted, seven to nine years old, 50% being female, with repaired unilateral cleft lip and palate (right or left), without associated malformations. Auditory skills were assessed using four central auditory processing tests: Random Gap Detection Test, Dichotic Digit Test, Dichotic Non-Verbal Test, Sustained Auditory Attention Ability Test. Language performance was evaluated by four standardized instruments: Illinois Psycholinguistic Skills Test, Peabody Picture Vocabulary Test, Token Test and Phonological Skills Profile. The association between auditory and language skills was evaluated by the Fisher exact test at a significance level of 5% (p<.05). RESULTS: The central auditory processing tests evidenced that only one child presented adequate performance in all skills analysed, five children presented impaired performance in all skills, and 16 exhibited deteriorations in one to three auditory skills, highlighting that temporal resolution was the most impaired skill (81%). Concerning language, three children presented adequate performance in all tests applied, and Visual Association and Auditory Association were the most impaired skills (40%). No association was observed between deteriorations in auditory and language skills. CONCLUSION: There was high occurrence of impairment of auditory skills, which compose the central auditory processing, as well as of language skills, with greatest impairment of receptive language.

Auditory and language skills in children with cleft lip and palate

Objectives: to investigate auditory and language skills in children with repaired cleft lip and palate. Methods: The sample was composed of 22 children registered at the hospital where the study was conducted, seven to nine years old, 50% being female, with repaired unilateral cleft lip and palate (right or left), without associated malformations. Auditory skills were assessed using four central auditory processing tests: Random Gap Detection Test, Dichotic Digit Test, Dichotic Non-Verbal Test, Sustained Auditory Attention Ability Test. Language performance was evaluated by four standardized instruments: Illinois Psycholinguistic Skills Test, Peabody Picture Vocabulary Test, Token Test and Phonological Skills Profile. The association between auditory and language skills was evaluated by the Fisher exact test at a significance level of 5% (p<.05). Results: The central auditory processing tests evidenced that only one child presented adequate performance in all skills analysed, five children presented impaired performance in all skills, and 16 exhibited deteriorations in one to three auditory skills, highlighting that temporal resolution was the most impaired skill (81%). Concerning language, three children presented adequate performance in all tests applied, and Visual Association and Auditory Association were the most impaired skills (40%). No association was observed between deteriorations in auditory and language skills. Conclusion: There was high occurrence of impairment of auditory skills, which compose the central auditory processing, as well as of language skills, with greatest impairment of receptive language.(AU)

Objetivos: Investigar las habilidades auditivas y lingüísticas en niños con labio leporino y paladar reparados. Métodos: La muestra se compuso de 22 niños registrados en el hospital en el que se realizó el estudio, de 7 a 9 años de edad, siendo el 50% niñas con labio leporino unilateral y paladar (derecho o izquierdo) reparados, sin malformaciones. Las habilidades auditivas se evaluaron utilizando 4 pruebas de procesamiento auditivo central: Random Gap Detection Test, Dichotic Digit Test, Dichotic Non-Verbal Test y Sustained Auditory Attention Ability Test. El desempeño lingüístico se evaluó utilizando diversos instrumentos estandarizados: Illinois Psycholinguistic Skills Test, Peabody Picture Vocabulary Test, Token Test y Phonological Skills Profile. La asociación entre las habilidades auditivas y lingüísticas se evaluó mediante la prueba exacta de Fisher, con un nivel de significación del 5% (p<0,05). Resultados: Las pruebas de procesamiento auditivo central evidenciaron que solo un niño presentó un desempeño adecuado en todas las habilidades analizadas, 5 niños presentaron una alteración del desempeño en todas las habilidades y 16 niños mostraron alteraciones en una de las 3 habilidades auditivas, subrayando que la resolución temporal fue la habilidad más deficiente (81%). Con relación al lenguaje, 3 niños presentaron un desempeño adecuado en todas las pruebas aplicadas, siendo las habilidades más deficientes la asociación visual y la asociación auditiva (40%). No se observó asociación entre las alteraciones de las habilidades auditivas y lingüísticas. Conclusión: Existió una alta incidencia de alteraciones de las habilidades auditivas que componen el procesamiento auditivo central, así como habilidades lingüísticas con gran alteración del lenguaje receptivo.(AU)

Social skills training in Speech-Language Pathology and Audiology: students' perception / Treinamento de habilidades sociais em Fonoaudiologia: percepção dos estudantes

ABSTRACT Purpose: to investigate the perception of Speech-Language Pathology and Audiology (SLPA) students, submitted to a Social Skills Training (SST) program, regarding potentialities, difficulties and perceived gains in their social skills (SS) repertoire. Methods: this qualitative study included 22 students (between 19 and 21 years old), enrolled in the 2nd year of the undergraduate SLPA course. The SST structure was based on theoretical-informative and practical-experiential methodology, developed over 15 meetings, using different teaching strategies. Content analysis was applied to assess the responses to a questionnaire with five open ended questions about the SS and the program itself, administered at the beginning, middle and end of the training. Results: greater difficulty was observed for students in relation to public speaking as well as empathetic and assertive skills toward their peers and professors. The participants highlighted the importance of the SST for the professional-patient relationship and for their professional training, as the training expands skills and competences beyond technical knowledge, with self-knowledge having a central role in this process. Conclusion: in preparation for clinical practice the SST can be used as a promising teaching-learning methodology in the curricula of SLPA courses.

RESUMO Objetivo: investigar a percepção de estudantes de Fonoaudiologia submetidos ao programa de Treinamento de Habilidades Sociais (THS) no que tange às potencialidades, dificuldades e ganhos percebidos no repertório de habilidades sociais (HS). Métodos: este estudo qualitativo incluiu 22 estudantes (idades entre 19 e 21 anos), matriculados no 2º ano do curso de graduação em Fonoaudiologia. A estrutura do THS baseou-se na metodologia teórico-informativa e prático-vivencial, desenvolvidas ao longo de 15 encontros, empregando-se distintas estratégias de ensino. A análise de conteúdo foi utilizada para avaliar as respostas a um questionário com cinco perguntas abertas a respeito das HS e do próprio programa, aplicado no início, meio e final do treinamento. Resultados: observou-se maior dificuldade dos participantes em falar em público e nas habilidades empáticas e assertivas com os colegas e professores. Os participantes destacaram a importância das HS na relação profissional-paciente e da inserção do programa para a formação profissional, por ampliar as habilidades e competências para além do saber técnico, tendo o autoconhecimento papel central neste processo. Conclusão: na preparação para a atividade clínica, o THS pode ser utilizado como uma metodologia de ensino-aprendizagem promissora nos currículos dos cursos de Fonoaudiologia.

Treinamento de habilidades sociais educativas com mães de pré-adolescentes com deficiência auditiva / Entrenamiento de habilidades sociales educativas con madres de preadolescentes con deficiencia auditiva / Training of educational social skills in mothers of preadolescents with hearing impairment

RESUMO. Desenvolveu-se um Programa de Treinamento de Habilidades Sociais Educativas com mães de pré-adolescentes com deficiência auditiva. Duas mães constituíram o Grupo Experimental (GE) e duas, o Controle (GC). Buscou-se avaliar os efeitos do Programa no repertório de comportamentos das mães e dos filhos por meio do Roteiro de Entrevista de Habilidades Sociais Educativas Parentais (RE-HSE-P) e o do Child Behavior Checklist (CBCL). Foi utilizado o método Jacobson Truax para análise dos dados do RE-HSE-P, obtendo mudanças confiáveis em relação ao incremento das habilidades sociais educativas positivas e das habilidades sociais infantis para o GE. Os dados do CBCL indicaram problemas de comportamento internalizantes no GE e em um participante do GC e problemas de comportamento externalizantes em um participante do GC na pré e na pós-intervenção e na avaliação follow up (para o GE). Acredita-se que o desenvolvimento de Programas nestes moldes pode se constituir em um importante aliado da fonoterapia.

RESUMEN. Se desarrolló un Programa de Entrenamiento de Habilidades Sociales Educativas con madres de preadolescentes con deficiencia auditiva. Dos madres constituyeron el Grupo Experimental (GE) y dos el Grupo Control (GC). Se buscó evaluar los efectos del Programa en el repertorio de comportamientos de las madres y de los hijos por medio de la Guía de Entrevista de Habilidades Sociales Educativas Parentales (GE-HSE-P) y de la Child Behavior Checklist (CBCL). Se utilizó el método Jacobson Truax para análisis de los datos del GE-HSE-P, obteniéndose cambios confiables en relación al incremento de las habilidades sociales educativas positivas y de las habilidades sociales infantiles para el GE. Los datos del CBCL indicaron problemas de comportamiento internalizantes en el GE y en un participante del GC y problemas de comportamiento externalizantes en un participante del GC en la pre y en la postintervención y en la evaluación follow up (para el GE). Se cree que el desarrollo de estos modelos de Programas pueda constituirse en un importante aliado de la fonoterapia.

ABSTRACT. A Parental Social Skills Program was conducted with mothers of preadolescents with hearing impairment. Two mothers were included in the Experimental Group (EG) and two in the Control Group (CG). The study evaluated the effects of the Program on the repertoire of behaviors of mothers and children using the Interview Script for Parental Social Skills (IS-PSS) and the Child Behavior Checklist (CBCL). The Jacobson Truax method was applied to analyze data of the RE-HSE-P, achieving reliable changes concerning the increment of positive educational social skills and child social skills for the EG. Data of the CBCL indicated internalizing behavior disorders in the EG and in one participant of CG, and externalizing behavior disorders in one participant of the CG before and after intervention and on the follow-up evaluation (for the EG). It is believed that the development of programs like this may constitute an important aid in auditory rehabilitation.

Auditory and language skills in children with cleft lip and palate.

OBJECTIVES: to investigate auditory and language skills in children with repaired cleft lip and palate. METHODS: The sample was composed of 22 children registered at the hospital where the study was conducted, seven to nine years old, 50% being female, with repaired unilateral cleft lip and palate (right or left), without associated malformations. Auditory skills were assessed using four central auditory processing tests: Random Gap Detection Test, Dichotic Digit Test, Dichotic Non-Verbal Test, Sustained Auditory Attention Ability Test. Language performance was evaluated by four standardized instruments: Illinois Psycholinguistic Skills Test, Peabody Picture Vocabulary Test, Token Test and Phonological Skills Profile. The association between auditory and language skills was evaluated by the Fisher exact test at a significance level of 5% (p<.05). RESULTS: The central auditory processing tests evidenced that only one child presented adequate performance in all skills analysed, five children presented impaired performance in all skills, and 16 exhibited deteriorations in one to three auditory skills, highlighting that temporal resolution was the most impaired skill (81%). Concerning language, three children presented adequate performance in all tests applied, and Visual Association and Auditory Association were the most impaired skills (40%). No association was observed between deteriorations in auditory and language skills. CONCLUSION: There was high occurrence of impairment of auditory skills, which compose the central auditory processing, as well as of language skills, with greatest impairment of receptive language.

Narrativas sobre a vida e o início do tratamento de uma paciente com Síndrome de Treacher Collins: um estudo de caso / Stories about life and treatment onset of a patient with Treacher Collins syndrome: case study

Síndrome de Treacher Collins (STC) é uma anomalia do desenvolvimento craniofacial rara de manifestação clínica variável. Este estudo teve por objetivo principal analisar a experiência de uma mulher de 26 anos com STC que iniciou a reabilitação na idade adulta, buscando aprofundar possíveis impactos para o seu desenvolvimento. Com aprovação do Comitê de Ética em Pesquisa (CAAE 00981418.3.0000.5441), realizou-se um estudo de caso clínico por meio da análise documental do prontuário multiprofissional e uma entrevista semiestruturada gravada em áudio, transcrita integralmente e analisada qualitativamente pela técnica de Análise de Conteúdo de Bardin. Evidenciaram-se duas categorias temáticas que sinalizam a experiência de vida da participante dividida em dois momentos: (1)"Desenvolvimento até a fase adulta" que abarcou as subcategorias: "O que eu tenho?"; "Relacionamento com a mãe"; "Eu sofri bullying: desafio da escolarização" (2) "Ser alguém com Síndrome de Treacher Collins", e subcategorias: "Existem outros como eu: conhecendo o diagnóstico"; "Início do tratamento: desafios e expectativas"; "A psicologia e a equipe interdisciplinar"; "Mas hoje eu sou feliz: planos para o futuro". STC, sendo uma malformação facial, pode implicar em conviver com o estigma de não apresentar o rosto dentro dos padrões sociais impostos. No caso analisado, apontou-se sofrimento emocional, sendo este intensificado pelo não pedido de ajuda. Por outro lado, o diagnóstico da síndrome possibilitou o processo de identificação com outros sujeitos acometidos, o início da reabilitação e a vivência de impactos positivos em sua qualidade de vida. A psicologia figurou como espaço de escuta e possibilidade de reflexão sobre o processo de reabilitação.

The Treacher Collins syndrome (TCS) is a rare anomaly of craniofacial development with variable clinical manifestation. The main goal of this study was to analyze the experience of a 26-year-old woman with TCS who initiated her rehabilitation in adulthood, aiming to deepen the possible impacts on her development. After approval by the Institutional Ethics Review Board (CAAE 00981418.3.0000.5441), the case study was conducted by documental analysis of the multiprofessional patient records and a semi-structured interview recorded in audio, transcribed in full and qualitatively analyzed by the Content Analysis technique of Bardin. Two theme categories were evidenced that indicated the life experience of the participant divided in two periods: (1) "Development up to adulthood", which included the subcategories: "What's wrong with me?"; "Relationship with the mother"; "I suffered bullying: challenge of school education" (2) "Being someone with Treacher Collins syndrome", and subcategories: "There are others like me: knowing the diagnosis"; "Treatment onset: challenges and expectations"; "Psychology and the interdisciplinary team"; "But I am happy today: plans for the future". Since TCS is a facial malformation, it may involve living with the stigma of not presenting a face within the imposed social standards. The present case presented emotional suffering, worsened because she did not ask for help. Conversely, the diagnosis of the syndrome allowed the process of identification with other affected individuals, the onset of rehabilitation and experience of positive impacts on her quality of life. Psychology participated as a space for hearing and possibility of reflecting about the rehabilitation process.

Effect of music education on the promotion of school performance in children. / Efeito da educação musical na promoção do desempenho escolar em crianças.

PURPOSE: This study investigated the effect of music education on the repertoire of school skills in children submitted and not to music education. METHODS: The study sample was composed of 80 children aged 8-12 years, of both genders, divided into two groups: 40 students submitted to music education (experimental) and 40 students not submitted to music education (control). Data were collected using the Social Skills Rating System (SSRS-BR) and the School Performance Test (SPT) questionnaire. The results were submitted to statistical analysis (paired sample t-test and repeated measures ANOVA) at a 5% significance level. RESULTS: Results showed statistically significant difference between the groups, evidencing improvement in school performance and academic competence in the children submitted to music education. CONCLUSION: The benefit brought by musical learning associated with different areas of education and health is of great relevance, representing an effective strategy in inclusive practice and promotion of physical and mental health in children.

OBJETIVO: Este estudo investigou o efeito da educação musical no repertório de habilidades escolares em crianças expostas e não expostas à educação musical. MÉTODO: Foram avaliadas 80 crianças, entre oito a doze anos, ambos os sexos, divididos em dois grupos: 40 alunos com educação musical (experimental) e 40 alunos sem educação musical (controle). Para coleta dos dados, foram utilizados o questionário do Sistema de Avaliação de Habilidades Sociais (SSRS-M) e o Teste de Desempenho Escolar (TDE). RESULTADOS: Indicaram diferença estatisticamente significante nas crianças expostas à educação musical, evidenciando que houve melhoria no desempenho escolar e na competência acadêmica. CONCLUSÃO: Portanto, é de grande relevância o benefício da aprendizagem musical aliada a diferentes áreas da educação e da saúde, uma vez que pode representar uma estratégia eficaz na prática inclusiva e na promoção da saúde física e mental das crianças.

A autoadvocacia como prática de empoderamento de adolescentes com deficiência auditiva: um estudo-piloto / Self-advocacy as a practice of empowering adolescents with hearing impairment: a pilot study

RESUMO Objetivo verificar a efetividade da intervenção com atividades lúdicas grupais que visam desenvolver a autoadvocacia e a autocidadania como prática de empoderamento de adolescentes com deficiência auditiva. Métodos trata-se de um estudo experimental pré e pós-intervenção, de abordagem quantitativa e qualitativa. Participaram quatro adolescentes com idades entre 12 e 17 anos, usuários de aparelho de amplificação sonora individual e/ou implante coclear, oralizados. Foram realizados cinco encontros presenciais, nos quais foram abordados temas relacionados à autoadvocacia, por meio de atividades lúdicas. Os instrumentos Checklist de Autoadvocacia "Eu consigo" e o Questionário de participação em sala de aula foram aplicados na pré e pós- intervenção. Foram aplicados o Inventário de Habilidades Sociais para Aadolescentes (IHS-Adolescente) e a Escala Wechsler Abreviada de Inteligência. Os dados foram analisados de forma qualitativa e quantitativa. Resultados No Inventário de Habilidades Sociais para Adolescentes, para frequência, todos os participantes foram classificados como abaixo da média ou média inferior. No teste de Escala Wechsler Abreviada de Inteligência, observando o dado de quociente de inteligência de execução, todos ficaram na média. Houve diferenças na comparação dos resultados pré e pós-intervenção do Checklist de Autoadvocacia "Eu consigo", principalmente no domínio compreensão da audição e da perda auditiva e uso dos dispositivos auditivos. No Questionário de participação em sala de aula, foi observada piora em alguns domínios, como compreensão dos professores e aspectos negativos. Conclusão O programa de intervenção com a estruturação proposta neste estudo foi eficiente para desenvolver as habilidades de autoadvocacia e autocidadania para o empoderamento de adolescentes com deficiência auditiva.

ABSTRACT Purpose To verify the effectiveness of an intervention with recreational activities that aim to develop self-advocacy and citizenship as a practice of empowerment for adolescents with hearing impairment. Methods This is a pre- and post-intervention experimental study with a quantitative and qualitative approach. Four oral hard-of-hearing adolescents aged between 12 and 17 years, users of hearing aids and/or cochlear implants, participated in this study. Five face-to-face meetings were held, in which topics related to self-advocacy were addressed through recreational activities. The Self-advocacy Checklist "I can" and the Classroom Participation Questionnaire (CPQ) were applied pre- and post-intervention. The Social Skills Inventory for Adolescents (IHSA-Del-Prette) and the Wechsler Abbreviated Scale of Intelligence (WASI) were also used. The data were analyzed utilizing qualitative and quantitative methods. Results In the Frequency Indicator of the IHSA-Del-Prette, all participants were classified as low average or below average. In the WASI, which analyzed performance IQ, all participants were classified as average. Differences were observed when comparing the Self-advocacy Checklist "I can" pre- and post-intervention, especially regarding hearing and hearing loss and the use of hearing devices. In the CPQ, worsening was observed in some domains, such as teachers' understanding and negative aspects. Conclusion The intervention program with the structure proposed in this study was efficient in developing self-advocacy and citizenship skills to empower adolescents with hearing impairment.

O uso de cenários cotidianos baseados na ferramenta educacional My World com mães de crianças e adolescentes com deficiência auditiva / The use of everyday scenarios based on the educational tool "My World" in mothers of children and adolescents with hearing loss

RESUMO Objetivo Identificar a concepção dos participantes sobre o uso dos cenários e personagens da ferramenta My World para o treinamento de habilidades sociais educativas cotidianas com mães de crianças e adolescentes com deficiência auditiva. Métodos Estudo exploratório sobre a análise dos relatos dos participantes quanto ao uso dos cenários e personagens da ferramenta para desenvolvimento de práticas parentais positivas. O estudo foi desenvolvido em uma clínica-escola de Fonoaudiologia de uma faculdade do interior do estado de São Paulo, Brasil, com três mães de crianças com deficiência auditiva, que realizavam terapia fonoaudiológica naquele local. Para coleta dos dados, foi aplicado um questionário sobre os elementos da ferramenta. Resultados Observou-se que os elementos da ferramenta parecem ter contribuído para que as mães identificassem mais concretamente dificuldades e facilidades na interação com seus filhos com deficiência auditiva. Conclusão Acredita-se que este estudo possa auxiliar na implantação de ferramentas que favoreçam a participação dos familiares no processo de reabilitação auditiva, contribuindo, assim, para maior probabilidade de sucesso terapêutico.

ABSTRACT Purpose To identify the participants' opinion about the use of scenarios and characters of the educational tool "My World", in parents of children with hearing loss. Methods This exploratory study analyzed the reports of participants about utilization of the tool's scenarios and characters for the development of positive parental practices. The study was conducted at a university speech-language pathology clinic in a city at the country side of the state of São Paulo, Brazil, on three mothers of children and adolescents with hearing loss, who received speech therapy at the clinic. Data were collected using a questionnaire about the tool elements. Results The tool elements seemed to contribute for the mothers to more precisely identify the ups and downs in the interaction with their children with hearing loss. Conclusion This study can aid the development of tools to favor the participation of family members in the auditory rehabilitation of their children, thus contributing to increase possibility of therapeutic success.

Syndromic craniosynostosis: neuropsycholinguistic abilities and imaging analysis of the central nervous system.

OBJECTIVE: To characterize patients with syndromic craniosynostosis with respect to their neuropsycholinguistic abilities and to present these findings together with the brain abnormalities. METHODS: Eighteen patients with a diagnosis of syndromic craniosynostosis were studied. Eight patients had Apert syndrome and 10 had Crouzon syndrome. They were submitted to phonological evaluation, neuropsychological evaluation and magnetic resonance imaging of the brain. The phonological evaluation was done by behavioral observation of the language, the Peabody test, Token test and a school achievement test. The neuropsychological evaluation included the WISC III and WAIS tests. RESULTS: Abnormalities in language abilities were observed and the school achievement test showed abnormalities in 66.67% of the patients. A normal intelligence quotient was observed in 39.3% of the patients, and congenital abnormalities of the central nervous system were observed in 46.4% of the patients. CONCLUSION: Abnormalities of language abilities were observed in the majority of patients with syndromic craniosynostosis, and low cognitive performance was also observed.

Syndromic craniosynostosis: neuropsycholinguistic abilities and imaging analysis of the central nervous system / Craniossinostoses sindrômicas: habilidades neuropsicolinguísticas e análise por imagem do sistema nervoso central

ABSTRACT Objective: To characterize patients with syndromic craniosynostosis with respect to their neuropsycholinguistic abilities and to present these findings together with the brain abnormalities. Methods: Eighteen patients with a diagnosis of syndromic craniosynostosis were studied. Eight patients had Apert syndrome and 10 had Crouzon syndrome. They were submitted to phonological evaluation, neuropsychological evaluation and magnetic resonance imaging of the brain. The phonological evaluation was done by behavioral observation of the language, the Peabody test, Token test and a school achievement test. The neuropsychological evaluation included the WISC III and WAIS tests. Results: Abnormalities in language abilities were observed and the school achievement test showed abnormalities in 66.67% of the patients. A normal intelligence quotient was observed in 39.3% of the patients, and congenital abnormalities of the central nervous system were observed in 46.4% of the patients. Conclusion: Abnormalities of language abilities were observed in the majority of patients with syndromic craniosynostosis, and low cognitive performance was also observed.

RESUMO Objetivo: Caracterizar as habilidades neuropsicolinguísticas de indivíduos com craniossinostoses sindrômicas e apresentar esses achados com as anomalias do sistema nervoso central. Métodos: Participaram do estudo 18 sujeitos com diagnóstico clínico de craniossinostose sindrômica, 44,4% com a síndrome de Apert e 55,6% síndrome de Crouzon. Todos os sujeitos foram submetidos a avaliação fonoaudiológica, psicológica e exames de ressonância magnética do encéfalo. A avaliação fonoaudiológica foi contemplada pela Observação Comportamental da Linguagem, Teste Peabody (TVIP), Teste Token e Teste de Desempenho Escolar (TDE); enquanto a psicológica utilizou a WISC-III e a WAIS. Resultados: Observou-se alteração nas habilidades de linguagem em todos os protocolos utilizados, sendo o TDE o que apresentou maior porcentagem de alteração (66,67%).A avaliação cognitiva evidenciou quociente de inteligência dentro da média em 39,3% dos sujeitos, enquanto que 46,4% apresentaram malformações congênitas do sistema nervoso central. Conclusão: Constatou-se alterações nas habilidades de linguagem na maioria dos sujeitos com craniossinostoses sindrômicas, bem como o baixo desempenho cognitivo.

Consideração da idade mental na avaliação do vocabulário expressivo de crianças com Síndrome de Down / Mental age in the evaluation of the expressive vocabulary of children with Down Syndrome

RESUMO Objetivo: verificar vocabulário expressivo de crianças com Síndrome de Down, comparar ao desempenho de crianças com desenvolvimento típico de mesmo gênero em dois pareamentos distintos: considerando idade cronológica e mental, separadamente, e determinar a influência da idade considerada na avaliação desta população. Métodos: cumpriram-se aspectos éticos. Participaram 14 com Síndrome de Down, idade cronológica entre 38 a 63 meses, 14 com desenvolvimento típico pareado por gênero e idade mental e 14 com desenvolvimento típico pareado por gênero e idade cronológica. Após entrevista, aplicou-se Teste de Linguagem Infantil ABFW-Vocabulário Parte B. Para pareamento da idade mental utilizou-se o teste Stanford Binet. Aplicação do teste paramétrico ANOVA, teste Kruskal-Walis e Teste Tukey, quando necessário. Resultados: verificou-se desempenho inferior das crianças com Síndrome de Down comparadas ao grupo pareado por idade cronológica para nomeação correta e não nomeação das figuras. Não houve diferença significante entre o grupo com Síndrome de Down e com desenvolvimento típico pareado por idade mental. Conclusão: as crianças com Síndrome de Down apresentaram vocabulário expressivo aquém do esperado para a idade cronológica, porém próximo ao esperado para a idade mental, permitindo inferir que a idade considerada na avaliação da linguagem desta população interfere na análise dos resultados encontrados.

ABSTRACT Purpose: to verify the expressive vocabulary of children with Down syndrome, compare it to the performance of children of both genders with typical development, in two distinct pairings: chronological and mental age, separately, and determine the influence of the age considered in this population evaluation. Methods: ethical aspects were met. The sample consisted of 42 children of both genders, 14 with Down syndrome, and chronological age between 38 and 63 months, 14 with typical development paired by gender and mental age, and 14 with typical development paired by gender and chronological age. An interview and the Child Language ABFW Vocabulary Test Part B were conducted. Statistical analysis was performed by applying the parametric ANOVA, the Kruskal-Wallis test and the Tukey`s test, whenever necessary. Results: children with Down syndrome showed a lower performance compared to those in the group paired by chronological age for correct naming and no naming of the figures. There was no significant difference between the group with Down syndrome and the group with typical development paired by mental age for any of the three skills evaluated. Conclusion: children with Down syndrome showed expressive vocabulary below the expected for their chronological age, but close to the expected for their mental age, allowing the inference that the age considered in the evaluation of the language of this population interferes in the analysis of the results found.

Receptive language and intellectual abilities in preterm children.

OBJECTIVE: The aim of this study was to examine the association between receptive vocabulary performance and intellectual quotient (IQ) in preterm born children compared to children born at term. METHOD: A total of 72 preschool-age children participated in the study. Participants were divided in four groups: EG-I, including 20 moderate to late preterm born children; EG-II, comprehending 16 extremely preterm born children; CG-I and CG-II with correspondingly 20 and 16 children born at term. EG-I and CG-I as well as EG-II and CG-II groups were matched according to gender, chronological age, and family SES. The mean age of children in each group was: EG-I and CG-I: 30.3months; EG-II and CG-II: 29.1months. The assessment information was collected using an anamnesis protocol, the Brazilian criterion of economic classification, the Peabody Picture Vocabulary Test, and the Stanford-Binet Intelligence Scale. RESULTS: Mean scores for receptive vocabulary were significantly lower in both preterm groups (EG-I and EG-II) than in the corresponding matched groups (CG-I and CG-II). However, no significant differences were found among the preterm groups. Moreover, high correlations between vocabulary and IQ scores were found in both preterm groups (EG-I and EG-II). In contrast, no significant correlations were found when analyses considered each group of full-term born children (CG-I and CG-II). CONCLUSION: Our findings indicate that prematurity status has an impact on receptive language performance and on the pattern of relationships between receptive vocabulary and general intellectual functioning.

Apert and Crouzon syndromes-Cognitive development, brain abnormalities, and molecular aspects.

Apert and Crouzon are the most common craniosynostosis syndromes associated with mutations in the fibroblast growth factor receptor 2 (FGFR2) gene. We conducted a study to examine the molecular biology, brain abnormalities, and cognitive development of individuals with these syndromes. A retrospective longitudinal review of 14 patients with Apert and Crouzon syndromes seen at the outpatient Craniofacial Surgery Hospital for Rehabilitation of Craniofacial Anomalies in Brazil from January 1999 through August 2010 was performed. Patients between 11 and 36 years of age (mean 18.29 ± 5.80), received cognitive evaluations, cerebral magnetic resonance imaging, and molecular DNA analyses. Eight patients with Apert syndrome (AS) had full scale intelligence quotients (FSIQs) that ranged from 47 to 108 (mean 76.9 ± 20.2), and structural brain abnormalities were identified in five of eight patients. Six patients presented with a gain-of-function mutation (p.Ser252Trp) in FGFR2 and FSIQs in those patients ranged from 47 to78 (mean 67.2 ± 10.7). One patient with a gain-of-function mutation (p.Pro253Arg) had a FSIQ of 108 and another patient with an atypical splice mutation (940-2A →G) had a FSIQ of 104. Six patients with Crouzon syndrome had with mutations in exons IIIa and IIIc of FGFR2 and their FSIQs ranged from 82 to 102 (mean 93.5 ± 6.7). These reveal that molecular aspects are another factor that can be considered in studies of global and cognitive development of patients with Apert and Crouzon syndrome (CS). © 2016 Wiley Periodicals, Inc.

Orofacial functions and quality of life in oral health in subjects with dentofacial deformity.

PURPOSE: To investigate the influence of the facial pattern in orofacial functions (OFFs) and quality of life (QoL), and their relationship in individuals with dentofacial deformities (DFD). METHODS: As approved by the Research Ethics Committee, 36 subjects, aged between 18 and 40 years, divided into three groups of seven female and five male participants, i.e., facial pattern I (n=12), pattern II (n=12) and pattern III (n=12), participated in this study. The OFFs were assessed using the MBGR protocol and QoL by the Oral Health Impact Profile (OHIP-14) questionnaire. Comparisons between OFFs and facial patterns were made using the Kruskal-Wallis test, and the correlation between the facial pattern and QoL by means of Spearman's test, considering a 5% significance level. RESULTS: A significant difference (p<0.05) was observed when comparing patterns I and II, and patterns I and III, with no difference between patterns II and III, neither in the OHIP-14 nor in the MBGR. A significant linear correlation (r=0.666; p<0.05) was verified between the MBGR and the OHIP-14, showing that the worse the OFFs, the worse the QoL. CONCLUSION: The facial pattern influenced the performance of the OFFs and the QoL in individuals presenting DFD, with a greater occurrence of changes for patterns II and III, and the worse the OFFs, the worse the QoL in cases with DFD.